Calciphylaxis cutis

Definition

A rare, life-threatening, non-inflammatory vasculopathy characterized clinically by progressive and painful skin lesions associated with calcification of cutaneous arterial microvessels. Calciphylaxis predominantly affects patients with end-stage kidney disease (ESKD) on dialysis.

Disease data

Classification

Clinical subtype

ORPHA code

280065

OMIM code

ICD10 code

E83.5

ICD11 code

EB90.42

*Soruce