Microphthalmia-microtia-fetal akinesia syndrome

Orpha code: 2547OMIM code:

Definition

A rare lethal multiple congenital anomalies/dysmorphic syndrome characterized by the association of fetal akinesia sequence, bilateral microphthalmia, microtia, and persistent truncus arteriosus. Additional dysmorphic features include prominent forehead, small nose, micrognathia, as well as camptodactyly and symphalangism. Contractures of large joints and micropenis have also been reported.

Disease data
Classification

Malformation syndrome

Synonyms
Thomas-Jewett-Raines syndrome
Zespół Thomasa, Jewetta i Rainesa
ORPHA code
2547
OMIM code
-
ICD10 code
Q68.8
ICD11 code
-

No additional description.

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