Microcephaly-cervical spine fusion anomalies syndrome

Orpha code: 2522OMIM code: 251250

Definition

Microcephaly-cervical spine fusion anomalies syndrome is characterized by microcephaly, facial dysmorphism (beaked nose, low-set ears, downslanting palpebral fissures, micrognathia), mild intellectual deficit, short stature, and cervical spine fusion anomalies producing spinal cord compression. It has been described in two brothers born to consanguineous parents. Transmission is likely to be autosomal recessive.

Disease data
Classification

Malformation syndrome

ORPHA code
2522
OMIM code
251250
ICD10 code
Q87.8
ICD11 code
LD20.2

No additional description.

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