Vestibular schwannoma

Orpha code: 252175OMIM code:

Definition

Vestibular schwannoma is a rare tumor of the posterior fossa originating in the Schwann cells of the vestibular transitional zone of the vestibulocochlear nerve that can be benign, small, slow growing and asymptomatic or large, faster growing and aggressive and potentially fatal, presenting with symptoms of hearing and balance impairment, vertigo, ataxia, headache and fifth, sixth or seventh cranial nerve dysfunction and facial numbness.

Disease data
Classification

Clinical subtype

Synonyms
Acoustic neurilemoma
Neurilemmoma nerwu słuchowego
Nerwiak nerwu słuchowego
Acoustic neurinoma
Acoustic neuroma
ORPHA code
252175
OMIM code
-
ICD10 code
D33.3
ICD11 code
2A02.3

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl