Neonatal intrahepatic cholestasis due to citrin deficiency

Orpha code: 247598OMIM code: 605814

Definition

A mild subtype of citrin deficiency characterized clinically by low birth weight, failure to thrive, transient intrahepatic cholestasis, multiple aminoacidemia, galactosemia, hypoproteinemia, hepatomegaly, decreased coagulation factors, hemolytic anemia, variable but mostly mild liver dysfunction, and hypoglycemia.

Disease data
Classification

Disease

Synonyms
NICCD
Cholestaza wewnątrzwątrobowa noworodków wywołana przez Niedobór cytrynianu
NICCD
Neonatal intrahepatic cholestasis caused by citrin deficiency
ORPHA code
247598
OMIM code
605814
ICD10 code
E72.2
ICD11 code
-

No additional description.

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