Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma. Disease data Classification Disease Synonyms Hemangioma-thrombocytopenia syndrome Zespół hemangioma-trombocytopenia ORPHA code 2330 OMIM code 141000 ICD10 code D18.0 ICD11 code KA8Y *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl