Alpha-thalassemia-myelodysplastic syndrome

Orpha code: 231401OMIM code: 300448

Definition

An acquired form of alpha-thalassemia characterized by a myelodysplastic syndrome (MDS) or more rarely a myeloproliferative disease (MPD) associated with hemoglobin H disease (HbH).

Disease data
Classification

Disease

Synonyms
ATMDS
ATMDS
Nabyta choroba HbH
Nabyta choroba hemoglobiny H
Acquired HbH disease
Acquired hemoglobin H disease
ORPHA code
231401
OMIM code
300448
ICD10 code
D56.0
ICD11 code
-

No additional description.

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