Jacobsen syndrome

Orpha code: 2308OMIM code: 147791

Definition

A rare genetic disorder caused by deletions in the long arm of chromosome 11 (<i>11q</i>) and mainly characterized by craniofacial dysmorphism, congenital heart disease, intellectual disability, Paris Trousseau bleeding disorder, structural kidney defects and immunodeficiency.

Disease data
Classification

Malformation syndrome

Synonyms
11q terminal deletion syndrome
Del(11)(q23.3)
Del(11)(qter)
Dystalna delecja 11q
Dystalna monosomia 11q
Monosomia 11qter
Telomerowa delecja 11q
Del(11)(q23.3)
Del(11)(qter)
Distal deletion 11q
Distal monosomy 11q
Monosomy 11qter
Telomeric deletion 11q
ORPHA code
2308
OMIM code
147791
ICD10 code
Q93.5
ICD11 code
LD44.B0

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl