Aortic arch interruption

Definition

A rare heart defect characterized by complete lack of anatomical continuity between the transverse aortic arch and the descending thoracic aorta. AAI should be distinguished anatomically from atresia of the aortic arch where continuity between these segments is achieved by an imperforate fibrous strand of various lengths.

Disease data

Classification

Morphological anomaly

ORPHA code

2299

OMIM code

ICD10 code

Q25.4

ICD11 code

LA8B.22

*Soruce