Adenoid cystic carcinoma of the cervix uteri

Orpha code: 213823OMIM code:

Definition

A rare, highly aggressive uterine cancer, macroscopically appearing as an irregular, slow-growing, non-friable, polypoid mass on the uterine cervix and histologically showing a pseudoglandular or cribriform growth pattern. It presents with vaginal bleeding and discharge and abdominal or pelvic pain. The tumor is highly infiltrative, often associated with vascular, lymphatic and perineural invasion, with subsequent haematogenous spread and early recurrence.

Disease data
Classification

Disease

Synonyms
Cervical adenoid cystic carcinoma
Rak gruczołowato-torbielowaty szyjki
ORPHA code
213823
OMIM code
-
ICD10 code
C53.8
ICD11 code
2C77.1

No additional description.

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