Infantile digital fibromatosis

Orpha code: 199267OMIM code:

Definition

A rare, benign, superficial fibromatosis characterized by firm, pinkish to flesh-colored, solitary or multiple nodular growths, typically less than 2 cm in size. They occur on the dorsal or lateral aspect of fingers and toes and have a tendency to recur. Histology reveals bland intradermal spindle cells with spherical perinuclear inclusion bodies.

Disease data
Classification

Disease

Synonyms
Inclusion body fibromatosis
Guz Reye'a
Nawracający dziecięcy guz włóknisty palców
Włókniakowatość z ciałkami wtrętowymi
Recurring digital fibrous tumor of childhood
Reye tumor
ORPHA code
199267
OMIM code
-
ICD10 code
M72.8
ICD11 code
EE61

No additional description.

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