Ulna metaphyseal dysplasia syndrome

Orpha code: 1837OMIM code: 191420

Definition

Ulna metaphyseal dysplasia syndrome is a rare primary bone dysplasia characterized by dysplasia of the distal ulnar metaphyses, as well as metacarpal/metatarsal dysplasia and metaphyseal changes resembling enchondromata. Patients usually present bony swelling of the wrists with or without pain (knees and ankles may also be affected). Other variably associated features include platyspondyly, skeletal development delay, short stature and coxa valga.

Disease data
Classification

Disease

Synonyms
Rosenberg-Lohr syndrome
Zespół Rosenberga i Lohra
ORPHA code
1837
OMIM code
191420
ICD10 code
Q78.5
ICD11 code
LD24.7

No additional description.

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