Ring chromosome 17 syndrome

Orpha code: 1441OMIM code:

Definicja

A rare chromosomal anomaly characterized by highly variable manifestations, ranging from a severe phenotype which presents with lissencephaly and severe intellectual disability to a milder phenotype that includes short stature, microcephaly, intellectual disability, seizures (that may be pharmacoresistant), café-au-lait spots, retinal flecks and minor facial dysmorphism, depending on the presence or absence of the Miller-Dieker critical region.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Ring 17
Ring chromosome 17
Kod ORPHA
1441
Kod OMIM
-
Kod ICD10
Q93.2
Kod ICD11
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl