Autosomal recessive palmoplantar keratoderma and congenital alopecia

Orpha code: 1366OMIM code: 212360

Definition

Autosomal recessive palmoplantar hyperkeratosis and congenital alopecia (PPK-CA) is a rare genetic skin disorder characterized by congenital alopecia and palmoplantar hyperkeratosis. It is usually associated with cataracts, progressive sclerodactyly and pseudo-ainhum.

Disease data
Classification

Disease

Synonyms
Autosomal recessive palmoplantar hyperkeratosis and congenital alopecia
Autosomalna recesywna hiperkeratoza dłoni i stóp z łysieniem wrodzonym
PPK-CA, typ Wallisa
Rogowiec dłoni i stóp z łysieniem wrodzonym, typ Wallisa
Zaćma - łysienie - sklerodaktylia
Cataract-alopecia-sclerodactyly syndrome
PPK-CA, Wallis type
Palmoplantar keratoderma and congenital alopecia, Wallis type
ORPHA code
1366
OMIM code
212360
ICD10 code
Q82.8
ICD11 code
LD27.0Y

No additional description.

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