Brachydactyly-arterial hypertension syndrome

Orpha code: 1276OMIM code: 112410

Definition

A rare genetic brachydactyly syndrome characterized by the association of brachydactyly type E with hypertension (due to vascular or neurovascular anomalies) as well as the additional features of short stature and low birth weight (compared to non-affected family members), stocky build and a round face. The onset of hypertension is often in childhood.

Disease data
Classification

Malformation syndrome

Synonyms
Bilginturan brachydactyly
Brachydaktylia Bilginturana
Brachydaktylia typu E z niskim wzrostem i nadciśnieniem
Zespół Bilginturana
Bilginturan syndrome
Brachydactyly type E, with short stature and hypertension
ORPHA code
1276
OMIM code
112410
ICD10 code
Q73.8
ICD11 code
LD24.8Y

No additional description.

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