Congenital atransferrinemia

Orpha code: 1195OMIM code: 209300

Definicja

Congenital atransferrinemia is a very rare hematologic disease caused by a transferrin (TF) deficiency and characterized by microcytic, hypochromic anemia (manifesting with pallor, fatigue and growth retardation) and iron overload, and that can be fatal if left untreated.

Disease data
Klasyfikacja

Disease

Synonimy
Congenital hypotransferrinemia
Wrodzona hipotransferynemia
Kod ORPHA
1195
Kod OMIM
209300
Kod ICD10
E88.0
Kod ICD11
5D0Y

No additional description.

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