Mixed cystic lymphatic malformation

Orpha code: 458792OMIM code:

Definition

A rare common cystic lymphatic malformation characterized by a benign cystic lesion composed of dilated lymphatic channels. Mixed cystic lesions consist of cysts both larger (macrocystic) and smaller (microcystic) than 1 cm in diameter. They usually present at birth or during the first years of life and most often occur in the head and neck region but may affect any site. Symptoms depend on the location and extent of the lesion. Infection, trauma, or intracystic hemorrhage can lead to lesional expansion. Malignant transformation does not occur.

Disease data
Classification

Malformation syndrome

Synonyms
Mixed cystic lymphangioma
Mieszany naczyniak limfatyczny torbielowaty
ORPHA code
458792
OMIM code
-
ICD10 code
D18.1
ICD11 code
-

No additional description.

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